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Hyperinsulinemic hypoglycemia 1

Congenital hyperinsulinism, nesidioblastosis is the most common cause of persistent hypoglycemia in infancy which is caused by increased insulin secretion despite of low blood glycose levels. The most important complication is cerebral damage as a result of prolonged hypoglycemia. Type 1 of the disease is caused by ABCC8 mutations.


Hyperinsulinemic hypoglycemia
Hyperinsulinemic hypoglycemia 1
Hyperinsulinemic hypoglycemia 2
Hyperinsulinemic hypoglycemia 3
Hyperinsulinemic hypoglycemia 4
Hyperinsulinemic hypoglycemia 5
Hyperinsulinemic hypoglycemia 6
Hyperinsulinemic hypoglycemia 7
Polycystic kidney disease with hyperinsulinemic hypoglycemia



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Glaser B et al. (1999) Neonatal Hyperinsulinism.

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Bianchi C et al. (1992) A case of familial nesidioblastosis: prenatal diagnosis of foetal hyperinsulinism.

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OMIM.ORG article

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Update: Aug. 14, 2020
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