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Nonpapillary renal cell carcinoma

Hypernephroma is a renal cell carcinoma with histomorphological characteristic clear cells. Often we find somatic mutations underlying this disease. However if those tumors occur at multiple sites and bilateral a germline mutation in the genes listed here has to be taken into account.

Systematic

Hereditary renal tumors
Hereditary leiomyomatosis and renal cell cancer
Hereditary papillary renal cell carcinoma
Nonpapillary renal cell carcinoma
DIRC2
FLCN
HNF1A
HNF1B
OGG1
RNF139
VHL
Wilms tumor
von Hippel-Lindau syndrome

References:

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OMIM.ORG article

Omim 144700 external link
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Wikipedia article

Wikipedia EN (Renal_cell_carcinoma) external link
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