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Mitochondrial diabetes

Mitochondrial diabetes is caused by mutations in genes that are inherited with mitochondria. Therefore these disorders show a maternal type of inheritance. The clinical picture is variable as it depends on the content of altered mitochondria. In a variable degree other organs might be affected.

Systematic

Diabetes mellitus
Diabetic nephropathy
Diabetic retinopathy
Gestational diabetes mellitus
Hereditary susceptibility to diabetes
Insulin resistance
MODY diabetes
Mitochondrial diabetes
MT-TE
MT-TK
MT-TL1
MT-TS2
Neonatal diabetes mellitus
Noninsulin-dependent diabetes mellitus 1
Pancreatogenic diabetes
Severe obesity and type 2 diabetes
Susceptibility to type 1 diabetes 01

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Orphanet article

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OMIM.ORG article

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Update: Aug. 14, 2020
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