Molekulargenetisches Labor
Zentrum für Nephrologie und Stoffwechsel

Lymphoproliferatives Syndrom

Das lymphoproliferatives Syndrom ist eine genetische Erkrankung bei welches die Apoptose gestört ist und es deshalb zu einer Akkumulation von Lymphozyten in verschiedenen Geweben kommen kann. Diese Proliferation lymphatischen Gewebes ist primär nicht maligne, kann aber sekundär zu Autoimmunprozessen und malignen Erkrankungen führen.

Gliederung

Hereditäre maligne Bluterkrankungen
Akute myeloische Leukämie
Erbliche Anfälligkeit für akute myeloische Leukämie
Erbliche Anfälligkeit für myelodysplastisches Syndrom
Juvenile myelomonozyäre Leukämie
Lymphoproliferatives Syndrom
Autoimmun-lymphoproliferatives Syndrom Typ 2
CASP10
Lymphoproliferatives Syndrom 1
ITK
X-chromosomales lymphoproliferatives Syndrom 1
SH2D1A
X-chromosomales lymphoproliferatives Syndrom 2
XIAP
Myelodysplastisches Syndrom
Non-Hodgkin-Lymphom
Noonan-Syndrom ähnliches Krankheitsbild und juvenile myelomonozytische Leukämie
Osteomyelofibrose
Polycythaemia vera
Somatische Erythrozytose

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2.

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50.

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51.

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52.

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53.

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Update: 8. Juni 2020