Die konotrunkalen Herzfehler betreffen den Ausflusstrakt des Herzens und umfassen Fallotsche Tetralogie, Truncus arteriosus communis, Pulmonalis-Atresie, rechter oder linker Doppelausstromventrikel und Transposition der großen Arterien. Sie machen etwa 30% aller angeborenen nicht-syndromalen Herzfehler aus.Es kommen verschiedene Vererbungsmuster vor und verschiedene Gene können betroffen sein.
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Orphanet article Orphanet ID 2445![]() |
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