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Dilatative Kardiomyopathie 1A

Die dilatative Kardiomyopathie 1A ist die häufigste Form der hereditären Kardiomyopathie. Die Vererbung ist autosomal dominant und Mutationen im LMNA-Gen sind ursächlich. Neben der Herzmuskelschwäche, die häufig nur mit Transplantation zu behandeln ist, finden sich auch Reizleitungsstörungen.

Gliederung

Hereditäre Kardiomyopathie
Dilatative Kardiomyopathie 1A
LMNA
Malouf-Syndrom

Referenzen:

1.

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OMIM.ORG article

Omim 115200 external link
Update: 14. August 2020
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