Erbliche Störungen des Complementsystems bestreffen die Proteine, welche die Komponenten eines Regulationssystems bilden. Störungen dieser Regulationssysteme können zu einer Abschwächung der Infektionsabwehr zu autoaggressiven Reaktonen führen.
1. |
Lipsker D et al. (2010) Cutaneous manifestations of complement deficiencies. |
2. |
None (2012) Complement genetics, deficiencies, and disease associations. |
3. |
Laursen NS et al. (2012) Structure, function and control of complement C5 and its proteolytic fragments. |
4. |
de Cordoba SR et al. (2012) Complement dysregulation and disease: from genes and proteins to diagnostics and drugs. |
5. |
None () Deficiencies and excessive human complement system activation in disorders of multifarious etiology. |
6. |
Grumach AS et al. (2014) Are complement deficiencies really rare? Overview on prevalence, clinical importance and modern diagnostic approach. |